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spondylocostal dysostosis 1
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DOID_0112365 |
[A spondylocostal dysostosis that has_material_basis_in homozygous or compound heterozygous mutation in the DLL3 gene on chromosome 19q13.2.] |
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spondylocostal dysostosis
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DOID_0050568 |
[A dysostosis that results_in abnormal development located_in vertebrae or located_in ribs. The bones of the spine do not develop properly, which causes them to be misshapen and abnormally joined together.] |
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spondylocostal dysostosis 4
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DOID_0112364 |
[A spondylocostal dysostosis that has_material_basis_in heterozygous or compound homozygous mutation in the HES7 gene on chromosome 17p13.1.] |
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hemochromatosis type 2
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DOID_0111034 |
[A hemochromatosis characterized by autosomal recessive inheritance of early onset of severe iron loading with symptoms including; hypogonadotropic hypogonadism, cardiomyopathy, arthropathy, and liver fibrosis or cirrhosis.] |
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spondylocostal dysostosis 5
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DOID_0112363 |
[A spondylocostal dysostosis that has_material_basis_in heterozygous, homozygous, or compound heterozygous mutation in the TBX6 gene on chromosome 16p11.2.] |
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hemochromatosis type 5
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DOID_0111031 |
[A hemochromatosis that has_material_basis_in heterozygous mutation in the FTH1 gene on chromosome 11q12.] |
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hemochromatosis type 2B
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DOID_0111032 |
[A hemochromatosis type 2 that has_material_basis_in homozygous mutation in the HAMP gene on chromosome 19q13.] |
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spondylocostal dysostosis 2
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DOID_0112362 |
[A spondylocostal dysostosis that has_material_basis_in homozygous or compound heterozygous mutation in the MESP2 gene on chromosome 15q26.1.] |
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glioma susceptibility 2
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MIM_613028 |
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spondylocostal dysostosis 3
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DOID_0112361 |
[A spondylocostal dysostosis that has_material_basis_in homozygous or compound heterozygous mutation in the LFNG gene on chromosome 7p22.3.] |
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glioma susceptibility 3
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MIM_613029 |
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hemochromatosis type 3
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DOID_0111030 |
[A hemochromatosis that has_material_basis_in homozygous or compound heterozygous mutation in the TFR2 gene on chromosome 7q22.] |
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spondylocostal dysostosis 6
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DOID_0112360 |
[A spondylocostal dysostosis that has_material_basis_in homozygous or compound heterozygous mutation in the RIPPLY2 gene on chromosome 6q14.2.] |
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exocrine pancreatic insufficiency
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DOID_13316 |
[A pancreas disease that is characterized by the inability of the exocrine pancreas to produce and secrete an adequate amount of digestive enzymes into the small intestine.] |
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hypermethioninemia with deficiency of S-adenosylhomocysteine hydrolase
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DOID_0111039 |
[A hypermethioninemia characterized by autosomal recessive inheritance of psychomotor delay, severe myopathy, hypermethioninaemia and elevated serum creatine kinase levels that has_material_basis_in compound heterozygous mutation in the AHCY gene on chromosome 20q11.] |
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hypermethioninemia
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DOID_0050544 |
[An amino acid metabolic disorder that involves an excess of the amino acid methionine, in the blood. This condition can occur when methionine is not broken down properly in the body.] |
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obsolete relapsing pancreatitis
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DOID_13315 |
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Coffin-Siris syndrome 7
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DOID_0112369 |
[A Coffin-Siris syndrome characterized by global developmental delay with mild to moderate intellectual disability, speech impairment, behavioral abnormalities, poor overall growth, coarse facial features, and hypoplastic fifth toenails that has_material_basis_in heterozygous mutation in the DPF2 gene on chromosome 11q13.1.] |
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glycine N-methyltransferase deficiency
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DOID_0111037 |
[A hypermethioninemia characterized by autosomal recessive inheritance of persistent isolated hypermethioninemia without cystathionine beta-synthase deficiency, tyrosinemia type I, or liver disease that has_material_basis_in homozygous or compound heterozygous mutation in the GNMT gene on chromosome 6p21.] |
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pancreatic mucinous ductal ectasia
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DOID_13313 |
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