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obsolete sulfuraminoacidemia
|
DOID_9264 |
|
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maple syrup urine disease
|
DOID_9269 |
[An organic acidemia that is caused by a deficiency of decarboxylase leading to high concentrations of valine, leucine, isoleucine, and alloisoleucine in the blood, urine, and cerebrospinal fluid and characterized by an odor of maple syrup to the urine, vomiting, hypertonicity, severe mental retardation, seizures, and eventually death unless the condition is treated with dietary measures.] |
|
organic acidemia
|
DOID_0060159 |
[An amino acid metabolic disorder that disrupts normal amino acid metabolism causing a building up of branched-chain amino acids.] |
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supraintestinal artery
|
UBERON_2005036 |
|
|
ion
|
CHEBI_24870 |
|
|
phenylketonuria
|
DOID_9281 |
[An amino acid metabolic disorder that is characterized by a mutation in the gene for the hepatic enzyme phenylalanine hydroxylase (PAH), rendering it nonfunctional.] |
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carbamoyl phosphate synthetase I deficiency disease
|
DOID_9280 |
[A urea cycle disorder that involves accumulation of ammonia in the blood.] |
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Clitoral hypertrophy
|
HP_0008665 |
|
|
Increased size of the clitoris
|
HP_0040253 |
|
|
Elevated circulating desmosterol concentration
|
HP_0034937 |
|
|
Abnormal circulating cholesterol concentration
|
HP_0003107 |
|
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Abnormality of the intrinsic pathway
|
HP_0010989 |
|
|
Abnormality of the coagulation cascade
|
HP_0003256 |
|
|
ocular hypertension
|
DOID_9282 |
[An eye disease that is characterized by elevated intraocular pressure in the absence of optic nerve damage or visual field loss.] |
|
hyperargininemia
|
DOID_9278 |
[An urea cycle disorder that involves arginase deficiency resulting in elevated levels of plasma arginine.] |
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primary cerebellar degeneration
|
DOID_9277 |
|
|
tyrosinemia
|
DOID_9275 |
[An amino acid metabolic disorder that involves impaired break down of the amino acid tyrosine.] |
|
tetrahydrofuranone
|
CHEBI_47016 |
|
|
oxolanes
|
CHEBI_26912 |
|
|
hyperhomocysteinemia
|
DOID_9279 |
[An amino acid metabolic disorder that involves an abnormally large level of homocysteine in the blood.] |