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Larsen-like syndrome B3GAT3 type
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DOID_0080575 |
[A syndrome that is characterized by laxity, dislocations and contractures of the joints, short stature, foot deformities (e.g. clubfeet), broad tips of fingers and toes, short neck, dysmorphic facial features (hypertelorism, downslanting palpebral fissures, upturned nose with anteverted nares, high arched palate) and various cardiac malformations and has_material_basis_in homozygous mutation in the B3GAT3 gene on chromosome 11q12.] |
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spondyloepimetaphyseal dysplasia, Genevieve-type
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DOID_0080576 |
[A spondyloepimetaphyseal dysplasia that is characterized by infantile-onset severe developmental delay and skeletal dysplasia, including short stature, premature carpal ossification, platyspondyly, longitudinal metaphyseal striations, and small epiphyses and has_material_basis_in homozygous or compound heterozygous mutation in the NANS gene on chromosome 9q22.] |
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obsolete tumor of the thecoma fibroma group
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DOID_5472 |
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intraorbital meningioma
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DOID_4141 |
[A meningioma by site and orbital neoplasm that is located_in the area around the eye sockets of the skull and results_in pressure in the eyes, giving a bulging appearance.] |
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orbital cancer
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DOID_4143 |
[A bone cancer that is located_in the area behind the eye and derives_from the orbit or secondarily derives_from an adjacent source (eyelid, paranasal sinus, or intracranial compartment). It results_in the eye pushing forward causing a bulging of the eye called proptosis.] |
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biliary dyskinesia
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DOID_4140 |
[A gallbladder disease characterized by altered tonus of the sphincter of Oddi, disturbance in the coordination of contraction of the biliary ducts, and/or reduction in the speed of emptying of the biliary tree.] |
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ovarian serous adenofibroma
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DOID_5474 |
[An ovarian benign neoplasm that has_material_basis_in glandular and fibrous tissues, with a relatively large proportion of glands and is characterized by the presence of serous fluid.] |
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orbital disease
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DOID_930 |
[An adnexa disease that is located_in the eye socket.] |
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obsolete meningioma by site
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DOID_4142 |
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cervical adenofibroma
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DOID_5476 |
[A cervical benign neoplasm that is has_material_basis_in glandular and fibrous tissues, with a relatively large proportion of glands.] |
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uterine corpus adenofibroma
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DOID_5475 |
[An uterine benign neoplasm that has_material_basis_in glandular and fibrous tissues, with a relatively large proportion of glands.] |
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obsolete herpes zoster dermatitis
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DOID_4144 |
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gastrointestinal adenoma
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DOID_4147 |
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fallopian tube adenofibroma
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DOID_5478 |
[A fallopian tube benign neoplasm that is has_material_basis_in glandular and fibrous tissues, with a relatively large proportion of glands.] |
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clear cell adenofibroma
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DOID_5477 |
[An adenofibroma that is characterized by the presence of cells with clear cytoplasm.] |
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blurred vision with haloes
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SYMP_0020010 |
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congenital disorder of glycosylation It
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DOID_0080570 |
[A congenital disorder of glycosylation I that is characterized by a wide range of clinical manifestations, most commonly presenting with bifid uvula with or without cleft palate at birth, associated with growth delay, hepatopathy with elevated aminotransferase serum levels, myopathy (including exercise-related fatigue, exercise intolerance, muscle weakness), intermittent hypoglycemia, and dilated cardiomyopathy and/or cardiac arrest, due to decreased phosphoglucomutase 1 enzyme activity and has_material_basis_in homozygous or compound heterozygous mutation in the PGM1 gene on chromosome 1p31.] |
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congenital disorder of glycosylation Iu
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DOID_0080571 |
[A congenital disorder of glycosylation I that is characterized by respiratory distress and severe hypotonia at birth, severe global developmental delay, early-onset intractable seizures, myopathic fascies with craniofacial dysmorphism (trigonocephaly/progressive microcephaly, low anterior hairline, arched eyebrows, hypotelorism, strabismus, small nose, prominent philtrum, thin upper lip, high-arched palate, micrognathia, malocclusion), severe, congenital flexion joint contractures and elevated serum creatine kinase levels and has_material_basis_in homozygous or compound heterozygous mutation in the DPM2 gene on chromosome 9q34.] |
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papillary adenofibroma
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DOID_5479 |
[An adenofibroma that is characterized by finger-like projections on histology.] |
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congenital disorder of glycosylation Iw
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DOID_0080572 |
[A congenital disorder of glycosylation I that is characterized by developmental delay, intellectual disability, failure to thrive, hypotonia and seizures and has_material_basis_in homozygous mutation in the STT3A gene on chromosome 11q24.] |