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leukocyte adhesion deficiency
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DOID_6612 |
[A combined T cell and B cell immunodeficiency that is characterized by defects affecting how white blood cells respond and travel to the site of a wound or infection affecting the immune system.] |
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ovarian dysgenesis 1
|
DOID_0080493 |
[A 46 XX gonadal dysgenesis that has_material_basis_in homozygous or compound heterozygous mutation in the gene encoding follicle-stimulating hormone receptor on chromosome 2p16.] |
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ovarian dysgenesis 2
|
DOID_0080494 |
[A 46 XX gonadal dysgenesis that has_material_basis_in mutation in the BMP15 gene on chromosome Xp11.] |
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ovarian dysgenesis 3
|
DOID_0080495 |
[A 46 XX gonadal dysgenesis that has_material_basis_in homozygous mutation in the PSMC3IP gene on chromosome 17q12-q21.] |
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mucolipidosis type IV
|
DOID_0080490 |
[A mucolipidosis that is characterized by delayed development and vision impairment that worsens over time.] |
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cerebral cavernous malformation 1
|
DOID_0080491 |
[A cerebral cavernous malformation that has_material_basis_in heterozygous mutation in the KRIT1 gene on chromosome 7q21.] |
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developmental and epileptic encephalopathy 2
|
DOID_0080467 |
[A developmental and epileptic encephalopathy characterized by X-linked dominant inheritance of seizure onset in the first months of life, intellectual disability, and poor motor control that has_material_basis_in mutation in the CDKL5 gene on chromosome Xp22.] |
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hemic and immune system symptom
|
SYMP_0017795 |
|
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developmental and epileptic encephalopathy 1
|
DOID_0080468 |
[A developmental and epileptic encephalopathy characterized by X-linked recessive inheritance of frequent tonic seizures or spasms beginning in infancy that has_material_basis_in mutation in the ARX gene on chromosome Xp21.] |
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obsolete congenital disorder of glycosylation type 2m
|
DOID_0080469 |
|
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developmental and epileptic encephalopathy 33
|
DOID_0080463 |
[A developmental and epileptic encephalopathy characterized by onset in the first months of life of seizures and severe global developmental delay with impaired intellectual development and poor or absent speech that has_material_basis_in heterozygous mutation in the EEF1A2 gene on chromosome 20q13.] |
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developmental and epileptic encephalopathy 53
|
DOID_0080464 |
[A developmental and epileptic encephalopathy characterized by infantile onset of intractable seizures, hypotonia, poor or absent global development, severe intellectual disability and spastic quadriplegia that has_material_basis_in homozygous or compound heterozygous mutation in the SYNJ1 gene on chromosome 21q22.] |
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developmental and epileptic encephalopathy 30
|
DOID_0080465 |
[A developmental and epileptic encephalopathy characterized by onset in the first few months of life of refractory seizures andseverely impaired or absent developmental progress that has_material_basis_in heterozygous mutation in the SIK1 gene on chromosome 21q22.] |
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obsolete multiple congenital anomalies-hypotonia-seizures syndrome 2
|
DOID_0080466 |
|
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chondroid chordoma
|
DOID_4152 |
[A chordoma that histologically derives_from chordoma, derives_from chondroma, and derives_from chondrosarcoma.] |
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synovial sarcoma
|
DOID_5485 |
[A synovium cancer which develops in the synovial membrane of the joints.] |
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synovium cancer
|
DOID_2706 |
|
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dentinogenesis imperfecta
|
DOID_4154 |
[A tooth disease characterized by discolored, opalescent teeth that has_material_basis_in mutation in the DSPP gene on chromosome 4q22.] |
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fibrous synovial sarcoma
|
DOID_5484 |
|
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spinal chordoma
|
DOID_4153 |
[A chordoma that derives_from the spine.] |